《英文msh詞典》Type Is,HSN
[入口詞] Type Is,HSN
[主題詞] Hereditary Sensory and Autonomic Neuropathies
[英文釋義] A group of inherited disorders characterized by degeneration of dorsal root and autonomic ganglion cells,and clinically by loss of sensation and autonomic dysfunction. There are five subtypes. Type I features autosomal dominant inheritance and distal sensory involvement. Type II is characterized by autosomal inheritance and distal and proximal sensory loss. Type III is DYSAUTONOMIA,FAMILIAL. Type IV features insensitivity to pain,heat intolerance,and mental deficiency. Type V is characterized by a selective loss of pain with intact light touch and vibratory sensation. (From Joynt,Clinical Neurology,1995,Ch51,pp142-4)